Hereditary Hemorrhagic Telangiectasia With Pulmonary Arteriovenous Fistulas
نویسندگان
چکیده
منابع مشابه
Asymptomatic pulmonary arteriovenous malformations in children with hereditary hemorrhagic telangiectasia.
BACKGROUND Children with Hereditary Hemorrhagic Telangiectasia (HHT) may have pulmonary arteriovenous malformations (AVMs), which can lead to symptoms of shortness of breath, exercise intolerance, clubbing, cyanosis and hemoptysis. However, some patients with pulmonary AVMs may be asymptomatic, placing them at risk for complications such as stroke or brain abscess if they are not identified and...
متن کاملLife-threatening pulmonary hemorrhage with pulmonary arteriovenous malformations and hereditary hemorrhagic telangiectasia.
The occurrence of significant pulmonary hemorrhage associated with pulmonary arteriovenous malformations (PAVMs) and hereditary hemorrhagic telangiectasia (HHT) and the incidence of PAVMs in family members of patients with PAVMs and HHT are poorly defined. We reviewed our experience in 143 patients with PAVMs and HHT. Eleven (8 percent) of the 143 patients with HHT and PAVMs had a history of ei...
متن کاملHereditary Hemorrhagic Telangiectasia with Atypical Pulmonary Arteriovenous Malformation during Advanced Pregnancy - A Case Report
We described a case of a new, atypical pulmonary arteriovenous malformation (AVM) during advanced pregnancy, in a previously well screened woman with known hereditary hemorrhagic telangiectasia (HHT) and a remote history of pulmonary AVM embolization. A 29-year old woman, gravida 3, para 2, at 35 weeks' gestation was admitted following a first episode of massive hemoptysis. Pulmonary angiograph...
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Hereditary hemorrhagic telangiectasia is a rare autosomal dominant inherited disease that is usually complicated by visceral vascular malformations. Patients harboring such malformations are at increased risk of brain abscess formation, which despite advances in diagnostic and surgical methods remains a life threatening medical emergency with high mortality and morbidity rates. In the present r...
متن کاملPulmonary arteriovenous malformations and embolic complications in patients with hereditary hemorrhagic telangiectasia.
Patients with hereditary hemorrhagic telangiectasia (HHT) and pulmonary arteriovenous malformation (PAVM) face higher risk of embolic complications. It is not clear whether poor outcomes are related to PAVM severity or pulmonary symptoms. Furthermore, there is currently no available data on HHT patients in Argentina. We conducted a cross sectional study in a teaching hospital in Buenos Aires, A...
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ژورنال
عنوان ژورنال: Circulation
سال: 2006
ISSN: 0009-7322,1524-4539
DOI: 10.1161/circulationaha.105.607507